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Kevin Southern

Professor Kevin Southern
MBChB, MRCP, FRCPCH, PhD

Contact

K.W.Southern@liverpool.ac.uk

+44 (0)151 228 4811 Ext. 3536

Publications

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2024

ECFS standards of care on CFTR-related disorders: Identification and care of the disorders.

Simmonds, N. J., Southern, K. W., De Wachter, E., De Boeck, K., Bodewes, F., Mainz, J. G., . . . ECFS Diagnostic Network Working Group. (2024). ECFS standards of care on CFTR-related disorders: Identification and care of the disorders.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 23(4), 590-602. doi:10.1016/j.jcf.2024.03.008

DOI
10.1016/j.jcf.2024.03.008
Journal article

ECFS standards of care on CFTR-related disorders: Towards a comprehensive program for affected individuals.

De Wachter, E., De Boeck, K., Sermet-Gaudelus, I., Simmonds, N. J., Munck, A., Naehrlich, L., . . . ECFS Diagnostic Network Working Group. (2024). ECFS standards of care on CFTR-related disorders: Towards a comprehensive program for affected individuals.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 23(3), 388-397. doi:10.1016/j.jcf.2024.01.012

DOI
10.1016/j.jcf.2024.01.012
Journal article

Standards for the care of people with cystic fibrosis (CF); recognising and addressing CF health issues.

Burgel, P. -R., Southern, K. W., Addy, C., Battezzati, A., Berry, C., Bouchara, J. -P., . . . Middleton, P. G. (2024). Standards for the care of people with cystic fibrosis (CF); recognising and addressing CF health issues.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, S1569-1993(24)00005-5. doi:10.1016/j.jcf.2024.01.005

DOI
10.1016/j.jcf.2024.01.005
Journal article

Letter to the editor: Risk of false newborn screening after intra-uterine exposure to ETI.

De Wachter, E., Davies, J. C., Simmonds, N. J., Castellani, C., de Winter-de Groot, K. M., Munck, A., . . . Barben, J. (2024). Letter to the editor: Risk of false newborn screening after intra-uterine exposure to ETI.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 23(1), 176-177. doi:10.1016/j.jcf.2023.07.003

DOI
10.1016/j.jcf.2023.07.003
Journal article

2023

CORRECTOR THERAPIES (WITH OR WITHOUT POTENTIATORS) FOR PEOPLE WITH CYSTIC FIBROSIS WITH CLASS II CFTR GENE VARIANTS (MOST COMMONLY F508DEL)

Heneohan, M., Southern, K. W., Murphy, J., Sinha, I. P., & Nevitt, S. J. (2022). CORRECTOR THERAPIES (WITH OR WITHOUT POTENTIATORS) FOR PEOPLE WITH CYSTIC FIBROSIS WITH CLASS II CFTR GENE VARIANTS (MOST COMMONLY F508DEL). In THORAX Vol. 77 (pp. A118-A119). Retrieved from https://www.webofscience.com/

Conference Paper

Standards for the care of people with cystic fibrosis (CF).

Southern, K. W., Burgel, P. -R., Castellani, C., De Boeck, K., Davies, J. C., Dunlevy, F., . . . van Koningsbruggen-Rietschel, S. (2023). Standards for the care of people with cystic fibrosis (CF).. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 22(6), 961-962. doi:10.1016/j.jcf.2023.09.009

DOI
10.1016/j.jcf.2023.09.009
Journal article

Standards for the care of people with cystic fibrosis (CF): A timely and accurate diagnosis.

Castellani, C., Simmonds, N. J., Barben, J., Addy, C., Bevan, A., Burgel, P. -R., . . . Southern, K. W. (2023). Standards for the care of people with cystic fibrosis (CF): A timely and accurate diagnosis.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 22(6), 963-968. doi:10.1016/j.jcf.2023.09.008

DOI
10.1016/j.jcf.2023.09.008
Journal article

Development and preliminary validation of the challenges of living with cystic fibrosis (CLCF) questionnaire: a 46-item measure of treatment burden for parent/carers of children with CF

Glasscoe, C., Hope, H. F., Lancaster, G. A., McCray, G., West, K., Patel, L., . . . Southern, K. W. (2023). Development and preliminary validation of the challenges of living with cystic fibrosis (CLCF) questionnaire: a 46-item measure of treatment burden for parent/carers of children with CF. PSYCHOLOGY & HEALTH, 38(10), 1309-1344. doi:10.1080/08870446.2021.2013483

DOI
10.1080/08870446.2021.2013483
Journal article

Development and validation of a short form psychometric tool assessing the caregiving Challenge of Living with Cystic Fibrosis (CLCF-SF) in a child

McCray, G., Hope, H. F. F., Glasscoe, C., Hill, J., Quittner, A., Southern, K. W. W., & Lancaster, G. A. A. (2023). Development and validation of a short form psychometric tool assessing the caregiving Challenge of Living with Cystic Fibrosis (CLCF-SF) in a child. PSYCHOLOGY & HEALTH. doi:10.1080/08870446.2023.2231489

DOI
10.1080/08870446.2023.2231489
Journal article

Raised Intracranial Pressure in Three Children with Cystic Fibrosis Receiving Elexacaftor-Tezacaftor-Ivacaftor Modulator Therapy.

Southern, K. W., Barben, J., Goldring, S., Kneen, R., Southward, S., Rajeev, Y., . . . Bush, A. (2023). Raised Intracranial Pressure in Three Children with Cystic Fibrosis Receiving Elexacaftor-Tezacaftor-Ivacaftor Modulator Therapy.. American journal of respiratory and critical care medicine. doi:10.1164/rccm.202303-0380le

DOI
10.1164/rccm.202303-0380le
Journal article

European survey of newborn bloodspot screening for CF: opportunity to address challenges and improve performance

Munck, A., Berger, D., Southern, K. W., Carducci, C., Groot, K. M. D. W. -D., Gartner, S., . . . Barben, J. (2023). European survey of newborn bloodspot screening for CF: opportunity to address challenges and improve performance. JOURNAL OF CYSTIC FIBROSIS, 22(3), 484-495. doi:10.1016/j.jcf.2022.09.012

DOI
10.1016/j.jcf.2022.09.012
Journal article

2022

ECFS standards of care on CFTR-related disorders: Updated diagnostic criteria

Castellani, C., De Boeck, K., De Wachter, E., Sermet-Gaudelus, I., Simmonds, N. J., & Southern, K. W. (2022). ECFS standards of care on CFTR-related disorders: Updated diagnostic criteria. JOURNAL OF CYSTIC FIBROSIS, 21(6), 908-921. doi:10.1016/j.jcf.2022.09.011

DOI
10.1016/j.jcf.2022.09.011
Journal article

Delivering Positive Newborn Screening Results: Cost Analysis of Existing Practice versus Innovative, Co-Designed Strategies from the ReSPoND Study

Fusco, F., Chudleigh, J., Holder, P., Bonham, J. R., Southern, K. W., Simpson, A., . . . Morris, S. (2022). Delivering Positive Newborn Screening Results: Cost Analysis of Existing Practice versus Innovative, Co-Designed Strategies from the ReSPoND Study. INTERNATIONAL JOURNAL OF NEONATAL SCREENING, 8(1). doi:10.3390/ijns8010019

DOI
10.3390/ijns8010019
Journal article

2021

Co-designing interventions for communicating positive newborn bloodspot screening results: use of online Experience-based Co-design (Preprint)

DOI
10.2196/preprints.33485
Preprint

Updated guidance on the management of children with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome/cystic fibrosis screen positive, inconclusive diagnosis (CRMS/CFSPID)

Barben, J., Castellani, C., Munck, A., Davies, J. C., De Winter-de Groot, K. M., Gartner, S., . . . Southern, K. W. (2021). Updated guidance on the management of children with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome/cystic fibrosis screen positive, inconclusive diagnosis (CRMS/CFSPID). JOURNAL OF CYSTIC FIBROSIS, 20(5), 810-819. doi:10.1016/j.jcf.2020.11.006

DOI
10.1016/j.jcf.2020.11.006
Journal article

Defining key outcomes to evaluate performance of newborn screening programmes for cystic fibrosis

Munck, A., Southern, K. W., Castellani, C., De Winter-de Groot, K. M., Gartner, S., Kashirskaya, N., . . . Barben, J. (2021). Defining key outcomes to evaluate performance of newborn screening programmes for cystic fibrosis. JOURNAL OF CYSTIC FIBROSIS, 20(5), 820-823. doi:10.1016/j.jcf.2021.02.006

DOI
10.1016/j.jcf.2021.02.006
Journal article

A systematic cochrane review of corrector therapies (with or without potentiators) for people with cystic fibrosis with class II gene variants (most commonly F508DEL).

Southern, K. W., Murphy, J., Sinha, I. P., & Nevitt, S. J. (n.d.). A systematic cochrane review of corrector therapies (with or without potentiators) for people with cystic fibrosis with class II gene variants (most commonly F508DEL).. Paediatric respiratory reviews. doi:10.1016/j.prrv.2021.03.001

DOI
10.1016/j.prrv.2021.03.001
Journal article

A survey of the prevalence, management and outcome of infants with an inconclusive diagnosis following newborn bloodspot screening for cystic fibrosis (CRMS/CFSPID) in six Italian centres

Terlizzi, V., Claut, L., Tosco, A., Colombo, C., Raia, V., Fabrizzi, B., . . . Padoan, R. (2021). A survey of the prevalence, management and outcome of infants with an inconclusive diagnosis following newborn bloodspot screening for cystic fibrosis (CRMS/CFSPID) in six Italian centres. JOURNAL OF CYSTIC FIBROSIS, 20(5), 828-834. doi:10.1016/j.jcf.2021.03.015

DOI
10.1016/j.jcf.2021.03.015
Journal article

Cystic fibrosis newborn screening: the importance of bloodspot sample quality

Doull, I., Course, C. W., Hanks, R. E., Southern, K. W., Forton, J. T., Thia, L. P., & Moat, S. J. (2021). Cystic fibrosis newborn screening: the importance of bloodspot sample quality. ARCHIVES OF DISEASE IN CHILDHOOD, 106(3), 253-257. doi:10.1136/archdischild-2020-318999

DOI
10.1136/archdischild-2020-318999
Journal article

2020

Processing of positive newborn screening results: a qualitative exploration of current practice in England

Chudleigh, J., Chinnery, H., Holder, P., Carling, R. S., Southern, K., Olander, E., . . . Simpson, A. (2020). Processing of positive newborn screening results: a qualitative exploration of current practice in England. BMJ OPEN, 10(12). doi:10.1136/bmjopen-2020-044755

DOI
10.1136/bmjopen-2020-044755
Journal article

Cystic fibrosis newborn screening for R117H in England

Dafydd, C., Moat, S., Southern, K. W., & Doull, I. J. M. (2020). Cystic fibrosis newborn screening for R117H in England. In EUROPEAN RESPIRATORY JOURNAL Vol. 56. doi:10.1183/13993003.congress-2020.2762

DOI
10.1183/13993003.congress-2020.2762
Conference Paper

Should the D1152H variant be included in cystic fibrosis newborn screening programmes?

Dafydd, C., Southern, K. W., Moat, S., & Doull, I. J. M. (2020). Should the D1152H variant be included in cystic fibrosis newborn screening programmes?. In EUROPEAN RESPIRATORY JOURNAL Vol. 56. doi:10.1183/13993003.congress-2020.2761

DOI
10.1183/13993003.congress-2020.2761
Conference Paper

Constructing a Bioethical Framework to Evaluate and Optimise Newborn Bloodspot Screening for Cystic Fibrosis

Armstrong, R. E., Frith, L., Ulph, F. M., & Southern, K. W. (2020). Constructing a Bioethical Framework to Evaluate and Optimise Newborn Bloodspot Screening for Cystic Fibrosis. International Journal of Neonatal Screening, 6(2). doi:10.3390/ijns6020040

DOI
10.3390/ijns6020040
Journal article

COVID-19 infection in children

Sinha, I. P., Harwood, R., Semple, M. G., Hawcutt, D. B., Thursfield, R., Narayan, O., . . . Southern, K. W. (2020). COVID-19 infection in children. LANCET RESPIRATORY MEDICINE, 8(5), 446-447. Retrieved from https://www.webofscience.com/

Journal article

2019

An open-label extension study of ivacaftor in children with CF and a <i>CFTR</i> gating mutation initiating treatment at age 2-5 years (KLIMB)

Rosenfeld, M., Cunningham, S., Harris, W. T., Lapey, A., Regelmann, W. E., Sawicki, G. S., . . . Davies, J. C. (2019). An open-label extension study of ivacaftor in children with CF and a <i>CFTR</i> gating mutation initiating treatment at age 2-5 years (KLIMB). JOURNAL OF CYSTIC FIBROSIS, 18(6), 838-843. doi:10.1016/j.jcf.2019.03.009

DOI
10.1016/j.jcf.2019.03.009
Journal article

Inconclusive diagnosis after a positive newborn bloodspot screening result for cystic fibrosis; clarification of the harmonised international definition.

Southern, K. W., Barben, J., Gartner, S., Munck, A., Castellani, C., Mayell, S. J., . . . Farrell, P. M. (2019). Inconclusive diagnosis after a positive newborn bloodspot screening result for cystic fibrosis; clarification of the harmonised international definition. JOURNAL OF CYSTIC FIBROSIS, 18(6), 778-780. doi:10.1016/j.jcf.2019.04.010

DOI
10.1016/j.jcf.2019.04.010
Journal article

Inhaled hypertonic saline for 3-6-year-olds with cystic fibrosis

Southern, K. W., & Sinha, I. P. (2019). Inhaled hypertonic saline for 3-6-year-olds with cystic fibrosis. LANCET RESPIRATORY MEDICINE, 7(9), 730-732. doi:10.1016/S2213-2600(19)30183-3

DOI
10.1016/S2213-2600(19)30183-3
Journal article

Adherence to Aerosol Therapy in Young People With Cystic Fibrosis: Patient and Parent Perspectives Following Electronic Data Capture

O'Toole, D. P. H., Latchford, G. J., Duff, A. J. A., Ball, R., McCormack, P., McNamara, P. S., . . . Southern, K. W. (2019). Adherence to Aerosol Therapy in Young People With Cystic Fibrosis: Patient and Parent Perspectives Following Electronic Data Capture. QUALITATIVE HEALTH RESEARCH, 29(6), 846-856. doi:10.1177/1049732318805754

DOI
10.1177/1049732318805754
Journal article

A systematic Cochrane Review of correctors (specific therapies for class II CFTR mutations) for cystic fibrosis [1]

Southern, K. W., Patel, S., Sinha, I. P., & Nevitt, S. J. (2019). A systematic Cochrane Review of correctors (specific therapies for class II CFTR mutations) for cystic fibrosis [1]. PAEDIATRIC RESPIRATORY REVIEWS, 30, 25-26. doi:10.1016/j.prrv.2019.01.003

DOI
10.1016/j.prrv.2019.01.003
Journal article

Rethinking Strategies for Positive Newborn Screening Result (NBS plus ) Delivery (ReSPoND): a process evaluation of co-designing interventions to minimise impact on parental emotional well-being and stress

Chudleigh, J., Bonham, J., Bryon, M., Francis, J., Moody, L., Morris, S., . . . Southern, K. (2019). Rethinking Strategies for Positive Newborn Screening Result (NBS plus ) Delivery (ReSPoND): a process evaluation of co-designing interventions to minimise impact on parental emotional well-being and stress. PILOT AND FEASIBILITY STUDIES, 5(1). doi:10.1186/s40814-019-0487-5

DOI
10.1186/s40814-019-0487-5
Journal article

2018

SEROLOGICAL CLASSIFICATION OF ASPERGILLUS DISEASE IN CHILDHOOD

Akinyemi, H. A., Mangat, S., Southern, K. W., Bedford, C., & McNamara, P. S. (2018). SEROLOGICAL CLASSIFICATION OF ASPERGILLUS DISEASE IN CHILDHOOD. In THORAX Vol. 73 (pp. A86-A87). doi:10.1136/thorax-2018-212555.145

DOI
10.1136/thorax-2018-212555.145
Conference Paper

A formative study exploring perceptions of physical activity and physical activity monitoring among children and young people with cystic fibrosis and health care professionals

Shelley, J., Fairclough, S. J., Knowles, Z. R., Southern, K. W., McCormack, P., Dawson, E. A., . . . Hanlon, C. (2018). A formative study exploring perceptions of physical activity and physical activity monitoring among children and young people with cystic fibrosis and health care professionals. BMC PEDIATRICS, 18. doi:10.1186/s12887-018-1301-x

DOI
10.1186/s12887-018-1301-x
Journal article

THE IMPACT OF NEWBORN SCREENING ON OUTCOMES AND INEQUALITIES IN CYSTIC FIBROSIS: A UK REGISTRY BASED STUDY

Schluter, D. K., Dryden, C., Southern, K. W., Diggle, P. J., & Taylor-Robinson, D. (2018). THE IMPACT OF NEWBORN SCREENING ON OUTCOMES AND INEQUALITIES IN CYSTIC FIBROSIS: A UK REGISTRY BASED STUDY. In JOURNAL OF EPIDEMIOLOGY AND COMMUNITY HEALTH Vol. 72 (pp. A27). doi:10.1136/jech-2018-SSMabstracts.55

DOI
10.1136/jech-2018-SSMabstracts.55
Conference Paper

2017

A mixed methods study of the administration of flucloxacillin oral liquid; identifying strategies to overcome administration issues of medicines with poor palatability.

Rouse, C., Mistry, P., Rayner, O., Nickless, J., Wan, M., Southern, K. W., & Batchelor, H. K. (2017). A mixed methods study of the administration of flucloxacillin oral liquid; identifying strategies to overcome administration issues of medicines with poor palatability. INTERNATIONAL JOURNAL OF PHARMACY PRACTICE, 25(5), 326-334. doi:10.1111/ijpp.12308

DOI
10.1111/ijpp.12308
Journal article

Ataluren and similar compounds (specific therapies for premature termination codon class I mutations) for cystic fibrosis

Aslam, A., Jahnke, N., Remmington, T., & Southern, K. W. (2017). Ataluren and similar compounds (specific therapies for premature termination codon class I mutations) for cystic fibrosis. PAEDIATRIC RESPIRATORY REVIEWS, 24, 32-34. doi:10.1016/j.prrv.2017.04.001

DOI
10.1016/j.prrv.2017.04.001
Journal article

Investigating the variation in the incidence of new Pseudomonas aeruginosa infection between paediatric cystic fibrosis centres.

Gilchrist, F. J., Jones, A. M., Smyth, A. R., Southern, K. W., Webb, A. K., & Lenney, W. (2017). Investigating the variation in the incidence of new Pseudomonas aeruginosa infection between paediatric cystic fibrosis centres.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 16(5), e14-e16. doi:10.1016/j.jcf.2017.06.006

DOI
10.1016/j.jcf.2017.06.006
Journal article

Cystic Fibrosis Transmembrane Conductance Regulator-Related Metabolic Syndrome and Cystic Fibrosis Screen Positive, Inconclusive Diagnosis.

Ren, C. L., Borowitz, D. S., Gonska, T., Howenstine, M. S., Levy, H., Massie, J., . . . Southern, K. W. (2017). Cystic Fibrosis Transmembrane Conductance Regulator-Related Metabolic Syndrome and Cystic Fibrosis Screen Positive, Inconclusive Diagnosis. JOURNAL OF PEDIATRICS, 181, S45-+. doi:10.1016/j.jpeds.2016.09.066

DOI
10.1016/j.jpeds.2016.09.066
Journal article

Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis Foundation.

Farrell, P. M., White, T. B., Ren, C. L., Hempstead, S. E., Accurso, F., Derichs, N., . . . Sosnay, P. R. (2017). Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis Foundation. JOURNAL OF PEDIATRICS, 181, S4-S15. doi:10.1016/j.jpeds.2016.09.064

DOI
10.1016/j.jpeds.2016.09.064
Journal article

Ataluren and similar compounds (specific therapies for premature termination codon class I mutations) for cystic fibrosis

Aslam, A. A., Higgins, C., Sinha, I. P., & Southern, K. W. (2017). Ataluren and similar compounds (specific therapies for premature termination codon class I mutations) for cystic fibrosis. Cochrane Database of Systematic Reviews. doi:10.1002/14651858.cd012040

DOI
10.1002/14651858.cd012040
Journal article

2016

Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis

Elphick, H. E., & Southern, K. W. (2016). Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (11). doi:10.1002/14651858.CD002204.pub4

DOI
10.1002/14651858.CD002204.pub4
Journal article

Pneumococcal vaccines for cystic fibrosis

Burgess, L., & Southern, K. W. (2016). Pneumococcal vaccines for cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (9). doi:10.1002/14651858.CD008865.pub4

DOI
10.1002/14651858.CD008865.pub4
Journal article

Safety, pharmacokinetics, and pharmacodynamics of ivacaftor in patients aged 2-5 years with cystic fibrosis and a CFTR gating mutation (KIWI): an open-label, single-arm study

Davies, J. C., Cunningham, S., Harris, W. T., Lapey, A., Regelmann, W. E., Sawicki, G. S., . . . Grp, K. I. W. I. S. (2016). Safety, pharmacokinetics, and pharmacodynamics of ivacaftor in patients aged 2-5 years with cystic fibrosis and a CFTR gating mutation (KIWI): an open-label, single-arm study. LANCET RESPIRATORY MEDICINE, 4(2), 107-115. doi:10.1016/S2213-2600(15)00545-7

DOI
10.1016/S2213-2600(15)00545-7
Journal article

2015

IVACAFTOR TREATMENT IN PRESCHOOL CHILDREN WITH CYSTIC FIBROSIS AND A CFTR GATING MUTATION: EXTENDED EVALUATION

Davies, J. C., Cunningham, S., Southern, K. W., Robertson, S., Green, Y., Cooke, J., . . . Rosenfeld, M. (2015). IVACAFTOR TREATMENT IN PRESCHOOL CHILDREN WITH CYSTIC FIBROSIS AND A CFTR GATING MUTATION: EXTENDED EVALUATION. In THORAX Vol. 70 (pp. A14). doi:10.1136/thoraxjnl-2015-207770.24

DOI
10.1136/thoraxjnl-2015-207770.24
Conference Paper

Cystic Fibrosis Screen Positive, Inconclusive Diagnosis (CFSPID): A new designation and management recommendations for infants with an inconclusive diagnosis following newborn screening

Munck, A., Mayell, S. J., Winters, V., Shawcross, A., Derichs, N., Parad, R., . . . Southern, K. W. (2015). Cystic Fibrosis Screen Positive, Inconclusive Diagnosis (CFSPID): A new designation and management recommendations for infants with an inconclusive diagnosis following newborn screening. Journal of Cystic Fibrosis, 14(6), 706-713. doi:10.1016/j.jcf.2015.01.001

DOI
10.1016/j.jcf.2015.01.001
Journal article

Social network analysis of <i>Pseudomonas aeruginosa</i> in cystic fibrosis

Taylor-Robinson, D. C., Southern, K. W., & Winstanley, C. (2015). Social network analysis of <i>Pseudomonas aeruginosa</i> in cystic fibrosis. LANCET RESPIRATORY MEDICINE, 3(8), 595-596. doi:10.1016/S2213-2600(15)00250-7

DOI
10.1016/S2213-2600(15)00250-7
Journal article

Topical nasal steroids for treating nasal polyposis in people with cystic fibrosis

Beer, H., Southern, K. W., & Swift, A. C. (2015). Topical nasal steroids for treating nasal polyposis in people with cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (6). doi:10.1002/14651858.CD008253.pub4

DOI
10.1002/14651858.CD008253.pub4
Journal article

Potentiators for cystic fibrosis - targeting the underlying molecular defect

Patel, S., Sinha, I. P., Dwan, K., Echevarria, C., Schechter, M., & Southern, K. W. (2015). Potentiators for cystic fibrosis - targeting the underlying molecular defect. PAEDIATRIC RESPIRATORY REVIEWS, 16(3), 162-164. doi:10.1016/j.prrv.2015.04.003

DOI
10.1016/j.prrv.2015.04.003
Journal article

Potentiators (specific therapies for class III and IV mutations) for cystic fibrosis

Patel, S., Sinha, I. P., Dwan, K., Echevarria, C., Schechter, M., & Southern, K. W. (2015). Potentiators (specific therapies for class III and IV mutations) for cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (03), 1-91. doi:10.1002/14651858.CD009841.pub2

DOI
10.1002/14651858.CD009841.pub2
Journal article

PERFORMANCE OF THE UK NEWBORN SCREENING PROGRAMME FOR CF, WHICH INCORPORATES STRATEGIES TO IMPROVE POSITIVE PREDICTIVE VALUE AND REDUCE CARRIER RECOGNITION

Southern, K. W., Morgan, T., Kour, S., Scott, E., Coppinger, C., Cavanagh, C., . . . Price, J. (2015). PERFORMANCE OF THE UK NEWBORN SCREENING PROGRAMME FOR CF, WHICH INCORPORATES STRATEGIES TO IMPROVE POSITIVE PREDICTIVE VALUE AND REDUCE CARRIER RECOGNITION. PEDIATRIC PULMONOLOGY, 50, 382-383. Retrieved from https://www.webofscience.com/

Journal article

2014

THE INCIDENCE OF NEW PSEUDOMONAS AERUGINOSA INFECTION IN CHILDREN WITH CYSTIC FIBROSIS

Gilchrist, F. J., Belcher, J., Jones, A. M., Smith, D., Smyth, A., Southern, K. W., . . . Lenney, W. (2014). THE INCIDENCE OF NEW PSEUDOMONAS AERUGINOSA INFECTION IN CHILDREN WITH CYSTIC FIBROSIS. In THORAX Vol. 69 (pp. A162-A163). doi:10.1136/thoraxjnl-2014-206260.326

DOI
10.1136/thoraxjnl-2014-206260.326
Conference Paper

Turnover of strains and intraclonal variation amongst <i>Pseudomonas aeruginosa</i> isolates from paediatric CF patients

Hall, A. J., Fothergill, J. L., McNamara, P. S., Southern, K. W., & Winstanley, C. (2014). Turnover of strains and intraclonal variation amongst <i>Pseudomonas aeruginosa</i> isolates from paediatric CF patients. DIAGNOSTIC MICROBIOLOGY AND INFECTIOUS DISEASE, 80(4), 324-326. doi:10.1016/j.diagmicrobio.2014.09.007

DOI
10.1016/j.diagmicrobio.2014.09.007
Journal article

Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis

Elphick, H. E., & Southern, K. W. (2014). Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (11). doi:10.1002/14651858.CD002204.pub3

DOI
10.1002/14651858.CD002204.pub3
Journal article

Pneumococcal vaccines for cystic fibrosis

Burgess, L., & Southern, K. W. (2014). Pneumococcal vaccines for cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (8). doi:10.1002/14651858.CD008865.pub3

DOI
10.1002/14651858.CD008865.pub3
Journal article

THE B LYMPHOCYTE DIFFERENTIATION FACTOR (BAFF) IS EXPRESSED IN THE AIRWAYS OF CHILDREN WITH CF AND IN LUNGS OF MICE INFECTED WITH PSEUDOMONAS AERUGINOSA

Neill, D. R., Saint, G. L., Bricio-Moreno, L., Fothergill, J., Southern, K. W., Winstanley, C., . . . Flanagan, B. F. (2014). THE B LYMPHOCYTE DIFFERENTIATION FACTOR (BAFF) IS EXPRESSED IN THE AIRWAYS OF CHILDREN WITH CF AND IN LUNGS OF MICE INFECTED WITH PSEUDOMONAS AERUGINOSA. PLoS One, 9(5). doi:10.1371/journal.pone.0095892.

DOI
10.1371/journal.pone.0095892.
Journal article

European Cystic Fibrosis Society Standards of Care: Best Practice guidelines

Smyth, A. R., Bell, S. C., Bojcin, S., Bryon, M., Duff, A., Flume, P., . . . Wolfe, S. (2014). European Cystic Fibrosis Society Standards of Care: Best Practice guidelines. JOURNAL OF CYSTIC FIBROSIS, 13(Supplement 1), S23-S42. doi:10.1016/j.jcf.2014.03.010

DOI
10.1016/j.jcf.2014.03.010
Journal article

Sodium channel blockers for cystic fibrosis.

Burrows, E. F., Southern, K. W., & Noone, P. G. (2014). Sodium channel blockers for cystic fibrosis.. The Cochrane database of systematic reviews, (4), CD005087. doi:10.1002/14651858.cd005087.pub4

DOI
10.1002/14651858.cd005087.pub4
Journal article

Considering consent: a structural equation modelling analysis of factors influencing decisional quality when accepting newborn screening

Nicholls, S. G., & Southern, K. W. (2014). Considering consent: a structural equation modelling analysis of factors influencing decisional quality when accepting newborn screening. JOURNAL OF INHERITED METABOLIC DISEASE, 37(2), 197-205. doi:10.1007/s10545-013-9651-x

DOI
10.1007/s10545-013-9651-x
Journal article

Correctors (specific therapies for class II CFTR mutations) for cystic fibrosis

Sinha, I. P., Southern, K. W., Dwan, K., & Patel, S. (n.d.). Correctors (specific therapies for class II CFTR mutations) for cystic fibrosis. Cochrane Database of Systematic Reviews. doi:10.1002/14651858.cd010966

DOI
10.1002/14651858.cd010966
Journal article

Gastrointestinal surgery in cystic fibrosis: A 20-year review

Farrelly, P. J., Charlesworth, C., Lee, S., Southern, K. W., & Baillie, C. T. (2014). Gastrointestinal surgery in cystic fibrosis: A 20-year review. JOURNAL OF PEDIATRIC SURGERY, 49(2), 280-283. doi:10.1016/j.jpedsurg.2013.11.038

DOI
10.1016/j.jpedsurg.2013.11.038
Journal article

Newborn screening for cystic fibrosis: opportunities and remaining challenges

Mehta, A., Sommerburg, O., & Southern, K. W. (2014). Newborn screening for cystic fibrosis: opportunities and remaining challenges. CYSTIC FIBROSIS, (64), 65-76. doi:10.1183/1025448x.10008913

DOI
10.1183/1025448x.10008913
Journal article

The challenge of improving outcomes for patients with CF sinonasal disease

VanDevanter, D. R., & Southern, K. W. (2014). The challenge of improving outcomes for patients with CF sinonasal disease. JOURNAL OF CYSTIC FIBROSIS, 13(4), 361-362. doi:10.1016/j.jcf.2014.05.014

DOI
10.1016/j.jcf.2014.05.014
Journal article

Variations in inflammation-related genes may be associated with childhood febrile seizure susceptibility

Emsley, H. C. A., Appleton, R. E., Whitmore, C. L., Jury, F., Lamb, J. A., Martin, J. E., . . . Allan, S. M. (2014). Variations in inflammation-related genes may be associated with childhood febrile seizure susceptibility. SEIZURE-EUROPEAN JOURNAL OF EPILEPSY, 23(6), 457-461. doi:10.1016/j.seizure.2014.03.006

DOI
10.1016/j.seizure.2014.03.006
Journal article

2013

Comparison of real time diagnostic chemistries to detect <i>Pseudomonas aeruginosa</i> in respiratory samples from cystic fibrosis patients

Fothergill, J. L., Ledson, M. J., Walshaw, M. J., McNamara, P. S., Southern, K. W., & Winstanley, C. (2013). Comparison of real time diagnostic chemistries to detect <i>Pseudomonas aeruginosa</i> in respiratory samples from cystic fibrosis patients. JOURNAL OF CYSTIC FIBROSIS, 12(6), 675-681. doi:10.1016/j.jcf.2013.04.007

DOI
10.1016/j.jcf.2013.04.007
Journal article

Adherence to nebulised therapies in adolescents with cystic fibrosis is best on week-days during school term-time

Ball, R., Southern, K. W., McCormack, P., Duff, A. J. A., Brownlee, K. G., & McNamara, P. S. (2013). Adherence to nebulised therapies in adolescents with cystic fibrosis is best on week-days during school term-time. JOURNAL OF CYSTIC FIBROSIS, 12(5), 440-444. doi:10.1016/j.jcf.2012.12.012

DOI
10.1016/j.jcf.2012.12.012
Journal article

Intraclonal genetic diversity amongst cystic fibrosis and keratitis isolates of Pseudomonas aeruginosa.

Hall, A. J., Fothergill, J. L., Kaye, S. B., Neal, T. J., McNamara, P. S., Southern, K. W., & Winstanley, C. (2013). Intraclonal genetic diversity amongst cystic fibrosis and keratitis isolates of Pseudomonas aeruginosa.. Journal of medical microbiology, 62(Pt 2), 208-216. doi:10.1099/jmm.0.048272-0

DOI
10.1099/jmm.0.048272-0
Journal article

After a long wait, two arrive, one after the other!

Southern, K. W., McCormack, P., & McNamara, P. S. (2013). After a long wait, two arrive, one after the other!. THORAX, 68(4), 311-312. doi:10.1136/thoraxjnl-2012-202891

DOI
10.1136/thoraxjnl-2012-202891
Journal article

CARERS COPE BETTER WITH THE DEMANDS OF CYSTIC FIBROSIS DURING TIMES OF ACUTE CARE; RESULTS FROM THE HOME INTRAVENOUS ANTIBIOTIC STUDY (H-IVAT)

Hope, H. F., Glasscoe, C., Nunn, T., Dale, C., Hill, J., & Southern, K. W. (2013). CARERS COPE BETTER WITH THE DEMANDS OF CYSTIC FIBROSIS DURING TIMES OF ACUTE CARE; RESULTS FROM THE HOME INTRAVENOUS ANTIBIOTIC STUDY (H-IVAT). In PEDIATRIC PULMONOLOGY Vol. 48 (pp. 438). Retrieved from https://www.webofscience.com/

Conference Paper

Intraclonal genetic diversity amongst cystic fibrosis and keratitis isolates of Pseudomonas aeruginosa

Hall, A. J., Fothergill, J. L., Kaye, S. B., Neal, T. J., McNamara, P. S., Southern, K. W., & Winstanley, C. (2013). Intraclonal genetic diversity amongst cystic fibrosis and keratitis isolates of Pseudomonas aeruginosa. Journal of Medical Microbiology, 62, 208-216.

Journal article

Parental Decision-Making and Acceptance of Newborn Bloodspot Screening: An Exploratory Study

Nicholls, S. G., & Southern, K. W. (2013). Parental Decision-Making and Acceptance of Newborn Bloodspot Screening: An Exploratory Study. PLOS ONE, 8(11). doi:10.1371/journal.pone.0079441

DOI
10.1371/journal.pone.0079441
Journal article

2012

New Nebulizer Technology to Monitor Adherence and Nebulizer Performance in Cystic Fibrosis

McCormack, P., Southern, K. W., & McNamara, P. S. (2012). New Nebulizer Technology to Monitor Adherence and Nebulizer Performance in Cystic Fibrosis. JOURNAL OF AEROSOL MEDICINE AND PULMONARY DRUG DELIVERY, 25(6), 307-309. doi:10.1089/jamp.2011.0934

DOI
10.1089/jamp.2011.0934
Journal article

Assessing the Liverpool Respiratory Symptom Questionnaire in children with cystic fibrosis

Trinick, R., Southern, K. W., & McNamara, P. S. (2012). Assessing the Liverpool Respiratory Symptom Questionnaire in children with cystic fibrosis. EUROPEAN RESPIRATORY JOURNAL, 39(4), 899-905. doi:10.1183/09031936.00070311

DOI
10.1183/09031936.00070311
Journal article

Mutation-specific therapies that potentiate cystic fibrosis transmembrane conductance regulator (CFTR) function in cystic fibrosis

Sinha, I. P., Southern, K. W., Dwan, K., Echevarria, C., & Schechter, M. (n.d.). Mutation-specific therapies that potentiate cystic fibrosis transmembrane conductance regulator (CFTR) function in cystic fibrosis. doi:10.1002/14651858.cd009841

DOI
10.1002/14651858.cd009841
Journal article

2011

Poster Session Abstracts

Poster Session Abstracts (2011). Pediatric Pulmonology, 46(S34), 212-428. doi:10.1002/ppul.21583

DOI
10.1002/ppul.21583
Journal article

A randomised controlled trial of breathing modes for adaptive aerosol delivery in children with cystic fibrosis

McCormack, P., McNamara, P. S., & Southern, K. W. (2011). A randomised controlled trial of breathing modes for adaptive aerosol delivery in children with cystic fibrosis. JOURNAL OF CYSTIC FIBROSIS, 10(5), 343-349. doi:10.1016/j.jcf.2011.04.006

DOI
10.1016/j.jcf.2011.04.006
Journal article

Array tube genotyping of Pseudomonas aeruginosa isolates as a strategy for identifying potential emerging transmissible strains.

Hall, A. J., Fothergill, J. L., Southern, K. W., McNamara, P. S., Ledson, M. J., Walshaw, M. J., & Winstanley, C. (2011). Array tube genotyping of Pseudomonas aeruginosa isolates as a strategy for identifying potential emerging transmissible strains.. Journal of Cystic Fibrosis, 10 (S1, S32.

Journal article

Comparison of real time diagnostic chemistries to detect early and chronic Pseudomonas aeruginosa colonisation in cystic fibrosis patients

Fothergill, J. L., Walshaw, M. J., Ledson, M. J., Southern, K. W., McNamara, P. S., & Winstanley, C. (2011). Comparison of real time diagnostic chemistries to detect early and chronic Pseudomonas aeruginosa colonisation in cystic fibrosis patients. Journal of Cystic Fibrosis, 10 (S1, S32.

Journal article

2010

Guidelines on the early management of infants diagnosed with cystic fibrosis following newborn screening.

Sermet-Gaudelus, I., Mayell, S. J., Southern, K. W., & European Cystic Finrosis Society (ECFS), Neonatal Screening Working Group. (2010). Guidelines on the early management of infants diagnosed with cystic fibrosis following newborn screening.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 9(5), 323-329. doi:10.1016/j.jcf.2010.04.008

DOI
10.1016/j.jcf.2010.04.008
Journal article

Components of risk associated with home intravenous antibiotic therapy (H-IVAT) in the UK

Glasscoe, C., Quittner, A. L., Patel, L., Dale, C., Burrows, E. F., Hope, H. F., . . . Nunn, A. J. (2010). Components of risk associated with home intravenous antibiotic therapy (H-IVAT) in the UK. Journal of Cystic Fibrosis, 9, S105. doi:10.1016/s1569-1993(10)60408-0

DOI
10.1016/s1569-1993(10)60408-0
Journal article

Microarray genotyping of Pseudomonas aeruginosa isolates from CF units

Hall, A. J., Fothergill, J. L., Southern, K. W., McNamara, P. S., Ledson, M. J., Walshaw, M. J., & Winstanley, C. (2010). Microarray genotyping of Pseudomonas aeruginosa isolates from CF units. Journal of Cystic Fibrosis, 9, S30. doi:10.1016/s1569-1993(10)60115-4

DOI
10.1016/s1569-1993(10)60115-4
Journal article

2009

Phenotypic characterisation of patients with intermediate sweat chloride values: towards validation of the European diagnostic algorithm for cystic fibrosis.

Goubau, C., Wilschanski, M., Skalická, V., Lebecque, P., Southern, K. W., Sermet, I., . . . De Boeck, K. (2009). Phenotypic characterisation of patients with intermediate sweat chloride values: towards validation of the European diagnostic algorithm for cystic fibrosis.. Thorax, 64(8), 683-691. doi:10.1136/thx.2008.104752

DOI
10.1136/thx.2008.104752
Journal article

Open adherence monitoring using routine data download from an adaptive aerosol delivery nebuliser in children with cystic fibrosis

McNamara, P. S., McCormack, P., McDonald, A. J., Heaf, L., & Southern, K. W. (2009). Open adherence monitoring using routine data download from an adaptive aerosol delivery nebuliser in children with cystic fibrosis. JOURNAL OF CYSTIC FIBROSIS, 8(4), 258-263. doi:10.1016/j.jcf.2009.04.006

DOI
10.1016/j.jcf.2009.04.006
Journal article

Estimating risk associated with home-based intravenous antibiotic therapy (IVAT)

Glasscoe, C., Southern, K. W., Lancaster, G. A., Quittner, A. L., Burrows, E. F., Heaf, L. J., . . . Nunn, A. J. (2009). Estimating risk associated with home-based intravenous antibiotic therapy (IVAT). Journal of Cystic Fibrosis, 8, S95. doi:10.1016/s1569-1993(09)60368-4

DOI
10.1016/s1569-1993(09)60368-4
Journal article

European best practice guidelines for cystic fibrosis neonatal screening.

Castellani, C., Southern, K. W., Brownlee, K., Dankert Roelse, J., Duff, A., Farrell, M., . . . Elborn, S. (2009). European best practice guidelines for cystic fibrosis neonatal screening.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 8(3), 153-173. doi:10.1016/j.jcf.2009.01.004

DOI
10.1016/j.jcf.2009.01.004
Journal article

Newborn screening for cystic fibrosis.

Southern, K. W., Mérelle, M. M. E., Dankert-Roelse, J. E., & Nagelkerke, A. D. (2009). Newborn screening for cystic fibrosis.. The Cochrane database of systematic reviews, (1), CD001402. doi:10.1002/14651858.cd001402.pub2

DOI
10.1002/14651858.cd001402.pub2
Journal article

A European consensus for the evaluation and management of infants with an equivocal diagnosis following newborn screening for cystic fibrosis.

Mayell, S. J., Munck, A., Craig, J. V., Sermet, I., Brownlee, K. G., Schwarz, M. J., . . . European Cystic Fibrosis Society Neonatal Screening Working Group. (2009). A European consensus for the evaluation and management of infants with an equivocal diagnosis following newborn screening for cystic fibrosis.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 8(1), 71-78. doi:10.1016/j.jcf.2008.09.005

DOI
10.1016/j.jcf.2008.09.005
Journal article

A reducing prevalence of the Liverpool Epidemic Strain of Pseudomonas aeruginosa in children attending the index paediatric clinic.

Morris, D., Fallon, L., Heaf, L., Burrows, E. F., Wallace, H., McNamara, P. S., . . . Southern, K. W. (2009). A reducing prevalence of the Liverpool Epidemic Strain of Pseudomonas aeruginosa in children attending the index paediatric clinic.. Ped Pulmonol, 32, 325.

Journal article

A reducing prevalence of the Liverpool Epidemic Strain of Pseudomonas aeruginosa in children attending the index paediatric clinic.

Morris, D., Fallon, L., Heaf, L., Burrows, E. F., Wallace, H., McNamara, P. N., . . . Southern, K. W. (2009). A reducing prevalence of the Liverpool Epidemic Strain of Pseudomonas aeruginosa in children attending the index paediatric clinic.. Pediatric Pulmonology, S32, 325.

Journal article

A reference interval for sweat chloride in infants aged between five and six weeks of age.

Jayaraj, R., Barton, P. V., Newland, P., Mountford, R., Shaw, N. J., McCarthy, E., . . . Southern, K. W. (2009). A reference interval for sweat chloride in infants aged between five and six weeks of age.. Annals of clinical biochemistry, 46(Pt 1), 73-78. doi:10.1258/acb.2008.008081

DOI
10.1258/acb.2008.008081
Journal article

2008

Embryonic lung growth is normal in a cftr-knockout mouse model.

Wallace, H. L., Connell, M. G., Losty, P. D., Jesudason, E. C., & Southern, K. W. (2008). Embryonic lung growth is normal in a cftr-knockout mouse model.. Experimental lung research, 34(10), 717-727. doi:10.1080/01902140802389719

DOI
10.1080/01902140802389719
Journal article

Airway ion transport impacts on disease presentation and severity in cystic fibrosis.

Leal, T., Fajac, I., Wallace, H. L., Lebecque, P., Lebacq, J., Hubert, D., . . . Southern, K. W. (2008). Airway ion transport impacts on disease presentation and severity in cystic fibrosis.. Clinical biochemistry, 41(10-11), 764-772. doi:10.1016/j.clinbiochem.2008.03.013

DOI
10.1016/j.clinbiochem.2008.03.013
Journal article

Challenge of Living with Cystic Fibrosis (CLCF): Psychometric evaluation

Glasscoe, C., Southern, K. W., Hope, H. F., Burrows, E., Heaf, L., Brownlee, K., . . . Quittner, A. L. (2008). Challenge of Living with Cystic Fibrosis (CLCF): Psychometric evaluation. In European CF Conference (pp. S96). Prague: Journal of Cystic Fibrosis.

Conference Paper

2007

Less is best? The impact of urokinase as the first line management of empyema thoracis.

Khalil, B. A., Corbett, P. A., Jones, M. O., Baillie, C. T., Southern, K., Losty, P. D., & Kenny, S. E. (2007). Less is best? The impact of urokinase as the first line management of empyema thoracis.. Pediatric surgery international, 23(2), 129-133. doi:10.1007/s00383-006-1806-5

DOI
10.1007/s00383-006-1806-5
Journal article

A survey of newborn screening for cystic fibrosis in Europe.

Southern, K. W., Munck, A., Pollitt, R., Travert, G., Zanolla, L., Dankert-Roelse, J., . . . ECFS CF Neonatal Screening Working Group. (2007). A survey of newborn screening for cystic fibrosis in Europe.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 6(1), 57-65. doi:10.1016/j.jcf.2006.05.008

DOI
10.1016/j.jcf.2006.05.008
Journal article

Achieving sustained compliance with nebulised therapies in a paediatric CF population

McCormack, P., MacDonald, A., Southern, K. S., & McNamara, P. S. (2007). Achieving sustained compliance with nebulised therapies in a paediatric CF population. Journal of Cystic Fibrosis, 6(June), S67.

Journal article

Challenges of Living with Cystic Fibosis (CLCF): Psychometric evaluation of a new measure

Glasscoe, C., Southern, K. W., Smith, J. A., Lancaster, G. A., Hill, J., Burrows, E. F., . . . Quittner, A. L. (2007). Challenges of Living with Cystic Fibosis (CLCF): Psychometric evaluation of a new measure. Pediatric Pulmonology, 30(Supp), 403.

Journal article

Electrical potential difference across the nasal epithelium is reduced in premature infants with chronic lung disease but is not associated with lower airway inflammation.

Gaillard, E. A., Shaw, N. J., Wallace, H. L., Vince, G., & Southern, K. W. (2007). Electrical potential difference across the nasal epithelium is reduced in premature infants with chronic lung disease but is not associated with lower airway inflammation.. Pediatric research, 61(1), 77-82. doi:10.1203/01.pdr.0000250035.10339.ce

DOI
10.1203/01.pdr.0000250035.10339.ce
Journal article

Living with Cystic Fibrosis Questionnaire (CFLC-Q): Development and preliminary validation of a new measure of the challenge experienced by caregivers

Glasscoe, C., Quittner, A. L., Smith, J. A., Burrows, E. F., Heaf, L., Cottrell, J., . . . Lancaster, G. A. (2007). Living with Cystic Fibrosis Questionnaire (CFLC-Q): Development and preliminary validation of a new measure of the challenge experienced by caregivers. Journal of Cystic Fibrosis, 6(Supp 1), S76.

Journal article

Significant findings on cranial CT scan after a first unprovoked seizure in children from North India.

Mathur, S., Southern, K., & Sharma, M. (2007). Significant findings on cranial CT scan after a first unprovoked seizure in children from North India.. Journal of Tropical Pediatrics, 56(6), 428-430.

Journal article

2006

Pulmonary edema in meningococcal septicemia associated with reduced epithelial chloride transport.

Eisenhut, M., Wallace, H., Barton, P., Gaillard, E., Newland, P., Diver, M., & Southern, K. W. (2006). Pulmonary edema in meningococcal septicemia associated with reduced epithelial chloride transport.. Pediatric critical care medicine : a journal of the Society of Critical Care Medicine and the World Federation of Pediatric Intensive and Critical Care Societies, 7(2), 119-124. doi:10.1097/01.pcc.0000200944.98424.e0

DOI
10.1097/01.pcc.0000200944.98424.e0
Journal article

A national survey of palivizumab for infants with cystic fibrosis

McCormick, J., & Southern, K. W. (2006). A national survey of palivizumab for infants with cystic fibrosis. Paediatric Pulmonology, Supp., 431.

Journal article

A systematic (Cochrane) review of topical sodium channel blockers for cystic fibrosis lung disease

Burrows, E. F., Noone, P. G., & Southern, K. W. (2006). A systematic (Cochrane) review of topical sodium channel blockers for cystic fibrosis lung disease. Paediatric Pulmonology, Supp., 355.

Journal article

Developing a tool to assess the impact on a family of caring for a child with cystic fibrosis

Glasscoe, C., Quittner, A. L., Evans, J., Burrows, E. F., Cottrell, J. J., Heaf, L., . . . Southern, K. W. (2006). Developing a tool to assess the impact on a family of caring for a child with cystic fibrosis. Pediatric Pulmonology, 29, 405-406.

Journal article

Establishing paediatric patients on an Adaptive Aerosol Delivery (AAD) device

McCormick, P., McDonald, A., & Southern, K. W. (2006). Establishing paediatric patients on an Adaptive Aerosol Delivery (AAD) device. Journal of Cystic Fibrosis, 5 (Sup, S76 (348).

Journal article

Reference range for sweat chloride in infants at 5-6 weeks of age

Jayaraj, R., Newland, P., Barton, P., Shaw, N. J., Isherwood, D., & Southern, K. W. (2006). Reference range for sweat chloride in infants at 5-6 weeks of age. Paediatric Pulmonology, Supp., 547.

Journal article

The challenge of living with cystic fibrosis: A collective response from parents

Glasscoe, C., Smith, J. A., Hope, H. F., Jones, S., Cottrell, J. J., Burrows, E. F., . . . Southern, K. W. (2006). The challenge of living with cystic fibrosis: A collective response from parents. Pediatric Pulmonology, 29, 406.

Journal article

Transition to adulthood for young people with CF

Hogan, J., Horgan, M., Southern, K., Cotrell, J., & Burrows, E. (2006). Transition to adulthood for young people with CF. Journal of Cystic Fibrosis, 5 (Sup, S87 (393.

Journal article

Use of exacerbation score to determine intravenous antibiotic use for acute respiratory exacerbations in Cystic Fibrosis

Das, D., Bako, O. L., Javadpour, S., Heaf, L. J., Southern, K. W., & Heaf, D. P. (2006). Use of exacerbation score to determine intravenous antibiotic use for acute respiratory exacerbations in Cystic Fibrosis. Journal of Cystic Fibrosis, 5 (Sup, S20 (91).

Journal article

Working in partnership with families to openly monitor aerosol therapy with an in-device data logger

McCormack, P., McDonald, A., Couriel, J. M., & Southern, K. W. (2006). Working in partnership with families to openly monitor aerosol therapy with an in-device data logger. Journal of Cystic Fibrosis, 5 (sup, S77 (352).

Journal article

2005

THYROID FUNCTION DURING SEVERE MENINGOCOCCAL SEPTICAEMIA

Eisenhut, M., Newland, P., & Southern, K. W. (2005). THYROID FUNCTION DURING SEVERE MENINGOCOCCAL SEPTICAEMIA. Pediatric Critical Care Medicine, 6(2), 239. doi:10.1097/00130478-200503000-00051

DOI
10.1097/00130478-200503000-00051
Journal article

A Survey on CF neonatal screening practice around Europe

Castellani, C., Dankert-Roelse, J., Munck, A., Pollitt, R., Southern, K. W., & Travert, G. (2005). A Survey on CF neonatal screening practice around Europe. Journal of Cystic Fibrosis, 4, S130.

Journal article

Chloride channel dysfunction associated with pulmonary oedema in meningococcal septicaemia

Eisenhut, M., Wallace, H. L., Barton, P., Gaillard, E., Newland, P., & Southern, K. W. (2005). Chloride channel dysfunction associated with pulmonary oedema in meningococcal septicaemia. Current Paediatrics, 15, 190-191.

Journal article

Does sputum induction (SI) increase recognition of an epidemic strain of Pseudomonas aeruginosa (PA)?

Wallace, H. L., McCormack, P., Jeffers, G., Heaf, D. P., Winstanley, C., Hart, C. A., & Southern, K. W. (2005). Does sputum induction (SI) increase recognition of an epidemic strain of Pseudomonas aeruginosa (PA)?. Journal of Cystic Fibrosis, 4, S42.

Journal article

Once versus three-times daily regimens of tobramycin treatment for pulmonary exacerbations of cystic fibrosis--the TOPIC study: a randomised controlled trial.

A, S., & et.al., F. T. T. S. G. (2005). Once versus three-times daily regimens of tobramycin treatment for pulmonary exacerbations of cystic fibrosis--the TOPIC study: a randomised controlled trial.. Lancet, 365(9459), 573-578. Retrieved from http://dx.doi.org/10.1016/S0140-6736(05)17906-9

Journal article

Sputum induction (SI) with 3% hypertonic saline in children

McCormack, P., Wallace, H. L., Heaf, D. P., & Southern, K. W. (2005). Sputum induction (SI) with 3% hypertonic saline in children. Journal of Cystic Fibrosis, 4, S100.

Journal article

Suitability of the upper airway models obtained from MRI studies in simulating drug lung deposition from inhalers.

Ehtezazi, T., Southern, K. W., Allanson, D., Jenkinson, I., & O'Callaghan, C. (2005). Suitability of the upper airway models obtained from MRI studies in simulating drug lung deposition from inhalers.. Pharmaceutical research, 22(1), 166-170. doi:10.1007/s11095-004-9023-1

DOI
10.1007/s11095-004-9023-1
Journal article

2004

Azithromycin for cystic fibrosis.

Southern, K. W., & Barker, P. M. (2004). Azithromycin for cystic fibrosis.. The European respiratory journal, 24(5), 834-838. doi:10.1183/09031936.04.00084304

DOI
10.1183/09031936.04.00084304
Journal article

Elevated sweat sodium associated with pulmonary oedema in meningococcal sepsis

Eisenhut, M., Sidaras, D., Barton, P., Newland, P., & Southern, K. W. (2004). Elevated sweat sodium associated with pulmonary oedema in meningococcal sepsis. Eur J Clin Invest, 34, 834-838.

Journal article

2003

Nasal airway ion transport and lung function in young people with cystic fibrosis.

Wallace, H. L., Barker, P. M., & Southern, K. W. (2003). Nasal airway ion transport and lung function in young people with cystic fibrosis.. American journal of respiratory and critical care medicine, 168(5), 594-600. doi:10.1164/rccm.200211-1302oc

DOI
10.1164/rccm.200211-1302oc
Journal article

Airway ion transport on the first postnatal day in infants delivered vaginally or by elective cesarean section.

Gaillard, E. A., Shaw, N. J., Wallace, H. L., Subhedar, N. V., & Southern, K. W. (2003). Airway ion transport on the first postnatal day in infants delivered vaginally or by elective cesarean section.. Pediatric research, 54(1), 58-63. doi:10.1203/01.pdr.0000069842.09976.cb

DOI
10.1203/01.pdr.0000069842.09976.cb
Journal article

Regulation of liquid secretion and absorption by the fetal and neonatal lung: basic mechanisms and role in neonatal lung disease

Barker, P. M., & Southern, K. W. (2003). Regulation of liquid secretion and absorption by the fetal and neonatal lung: basic mechanisms and role in neonatal lung disease. In R. A. Polin, W. W. Fox, & S. H. Abman (Eds.), Fetal and Neonatal Physiology (pp. 822-834). Penn: Saunders.

Chapter

2002

Airway surface liquid recovered by lavage with perfluorocarbon liquid in cats.

Southern, K. W., Funkhouser, W. K., Kazachkova, I., Godfrey, V. L., Fordham, L. A., Gatzy, J. T., & Barker, P. M. (2002). Airway surface liquid recovered by lavage with perfluorocarbon liquid in cats.. European journal of clinical investigation, 32(12), 956-961. doi:10.1046/j.1365-2362.2002.01100.x

DOI
10.1046/j.1365-2362.2002.01100.x
Journal article

2001

A modified technique for measurement of nasal transepithelial potential difference in infants.

Southern, K. W., Noone, P. G., Bosworth, D. G., Legrys, V. A., Knowles, M. R., & Barker, P. M. (2001). A modified technique for measurement of nasal transepithelial potential difference in infants.. The Journal of pediatrics, 139(3), 353-358. doi:10.1067/mpd.2001.116278

DOI
10.1067/mpd.2001.116278
Journal article

2000

Macrolide antibiotics for cystic fibrosis.

Southern, K. W., Barker, P. M., & Solis, A. (2000). Macrolide antibiotics for cystic fibrosis.. The Cochrane database of systematic reviews, (3), CD002203. doi:10.1002/14651858.cd002203

DOI
10.1002/14651858.cd002203
Journal article

1995

Generation and characterization of a delta F508 cystic fibrosis mouse model.

Colledge, W. H., Abella, B. S., Southern, K. W., Ratcliff, R., Jiang, C., Cheng, S. H., . . . Evans, M. J. (1995). Generation and characterization of a delta F508 cystic fibrosis mouse model.. Nature genetics, 10(4), 445-452. doi:10.1038/ng0895-445

DOI
10.1038/ng0895-445
Journal article